hipertensi pulmonal upn 2015

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    IPERTENSI

    IPERTENSI

    PULMONALULMONAL

    Prof.DR.dr.ZAINAL MUSTHAFA,MSi.,FS.,SpJP,FIHAProf.DR.dr.ZAINAL MUSTHAFA,MSi.,FS.,SpJP,FIHA

    Dep. Kardiologi RSPAD-GSDep. Kardiologi RSPAD-GS

    FK-UPN !e"era#$ Ja%ar"aFK-UPN !e"era#$ Ja%ar"a

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    PA

    PA

    Re&i&"e#&i A. P'l(o#ali&Re&i&"e#&i A. P'l(o#ali&

    Gagal Ja#"'#g Ka#a#Gagal Ja#"'#g Ka#a#

    Ke(a"ia# (e#dada%Ke(a"ia# (e#dada%

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    Proses Selulerroses Seluler

    PA

    PA

    Di&f'#g&i )#do"*elDi&f'#g&i )#do"*el

    Ke&ei(+a#ga# +ioa%"if al Ke&ei(+a#ga# +ioa%"if al Ni"ro'& ide /N0Ni"ro'& ide /N0

    Pro&"a&i%li#Pro&"a&i%li#

    T*ro(+oa# AT*ro(+oa# A11 )#do"*eli'( 2 3)#do"*eli'( 2 3

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    GANGGUAN

    ANGGUAN

    F'#g&i %a#al K 4 NaF'#g&i %a#al K 4 Na

    )pre&i "ra#&por &ero"o#i#)pre&i "ra#&por &ero"o#i#

    Prod'%&i (a"ri (e#i#g%a" /T'#i%a.ad!0Prod'%&i (a"ri (e#i#g%a" /T'#i%a.ad!0

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    KLASIFIKASI PALASIFIKASI PA

    3.3. Idiopa"i%Idiopa"i%

    1.1. Fa(ilialFa(ilial

    5.5. 6er*'+'#ga# de#ga#6er*'+'#ga# de#ga# Pe#7a%i" Jari#ga#Pe#7a%i" Jari#ga#

    PJ6PJ6

    Hiper"e#&i Por"alHiper"e#&i Por"al Pe#gar'* o+a" 4 Toi#Pe#gar'* o+a" 4 Toi#

    Lai#-lai#Lai#-lai#

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    KLASIFIKASI PA -------2

    LASIFIKASI PA -------2

    8.8. HPA a%i+a" pe#7a%i" Ja#"'#g KiriHPA a%i+a" pe#7a%i" Ja#"'#g Kiri Ga#gg'a# f'#g&i A"ri'( 4 !e#"ri%el %iriGa#gg'a# f'#g&i A"ri'( 4 !e#"ri%el %iri

    Ga#gg'a# %a"'p 9a#"'#g %iriGa#gg'a# %a"'p 9a#"'#g %iri

    :.:. HPA a%i+a" pe#7a%i" Par' 4 Hipo%&iaHPA a%i+a" pe#7a%i" Par' 4 Hipo%&ia PPMPPM

    Pe#7a%i" par' i#"re&"i"ialPe#7a%i" par' i#"re&"i"ial

    Ga#gg'a# "id'rGa#gg'a# "id'r Hipo!e#"ila&i al!eoliHipo!e#"ila&i al!eoli

    Ke"i#ggia#Ke"i#ggia#

    Kelai#a# per"'(+'*a#Kelai#a# per"'(+'*a#

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    KLASIFIKASI PA -------3

    LASIFIKASI PA -------3

    ;. HPA a%i+a" "*ro(+o e(+oli;. HPA a%i+a" "*ro(+o e(+oli

    )(+oli p'l(o#al)(+oli p'l(o#al

    )(+oli #o# "*ro(+o& /"'(or,para&i",+e#da)(+oli #o# "*ro(+o& /"'(or,para&i",+e#da

    a&i#g0a&i#g0

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    PATOGENESIS PA

    ATOGENESIS PA

    M'l"ifa%"orial, a.l. M'l"ifa%"orial, a.l.

    !a&o %o#"ra%&i!a&o %o#"ra%&i

    re(odelli#gre(odelli#g

    o+&"r'%&i pe(+'l'* dara*o+&"r'%&i pe(+'l'* dara*

    i#fla(a&i da# "*ro(+o&i&i#fla(a&i da# "*ro(+o&i&

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    CURIGAURIGA

    K)LUHAN 4 GANGGUANK)LUHAN 4 GANGGUAN

    &e&a% "a#pa %elai#a# 7a#g lai#&e&a% "a#pa %elai#a# 7a#g lai#

    >epa" lela*>epa" lela*

    le(a*le(a*

    a#gi#aa#gi#a&7#>ope&7#>ope

    di&"e#&i a+do(e#di&"e#&i a+do(e#

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    DETEKSI PAETEKSI PA

    )KG)KG

    Fo"o T*oraFo"o T*ora

    )%*o%ardiograp*7)%*o%ardiograp*7

    A#giograp*7A#giograp*7

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    KLASIFIKASI KLINISLASIFIKASI KLINIS

    Te&" f'#g&i par'Te&" f'#g&i par'AGDAGD

    =T=T

    A#giograp*7A#giograp*7

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    PENETUAN TYPEENETUAN TYPE

    LA6. DARAH 4 IMUNLGILA6. DARAH 4 IMUNLGI

    USG A6DM)NUSG A6DM)N

    TR)ADMILL T)STR)ADMILL T)S

    AGIGRAPH?AGIGRAPH?6IPS?6IPS?

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    Dx PA

    x PA

    Die!"##"$ie!"##"$( PAP @ 5 ((Hg( PAP @ 5 ((Hg

    PBPPBP 15 mmHg 15 mmHg

    PWR > 3PWR > 3

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    TATALAKSANA

    ATALAKSANA

    UMUMUMUM

    +a"a&i a%"ifi"a&+a"a&i a%"ifi"a&

    *i#dari %e"i#ggia#*i#dari %e"i#ggia#

    >ega* i#fla&i>ega* i#fla&i

    >ega* a#e(ia 4 H+>ega* a#e(ia 4 H+o+a"-o+a"a# 4o+a"-o+a"a# 4

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    O%AT

    %AT

    ANTI KAGULANANTI KAGULAN

    DIUR)TIKDIUR)TIK

    KSIG)NASIKSIG)NASI

    INTRPIKINTRPIK

    ==6 4 CASDILATASI==6 4 CASDILATASICAS DILATASICAS DILATASI

    DLLDLL

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    INTER&ENSI

    NTER&ENSI

    6ALN6ALN

    TRANSPLANTASITRANSPLANTASI

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