pp thalasemia refrat wilma
TRANSCRIPT
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Oleh : Wilma Pratiwi030.05.234
Fakultas KedokteranUniversitas Trisakti
Pemimin! :dr. "hristo#el. P$ %&.O'
THALASEMIA PADA
KEHAMILAN
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P()*+,U-U+)
Yunani
(talassa) laut.
Pertama kalidikenal di
sekitar LautTengah
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anakanak!
Anemia ! "em#esaranlim"a
setelah #erusia $tahun
*okter di
*etroit U%+Tahun /25
ANEMIA
%&&LEY
*r. enton"oole
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(P*(O-O'T,+-+%(+
$''.''' #aidilahirkan denganthalasemia "arah
tia" tahun di dunia
(Arthur Schoenstadt,
2008)
(Arthur Schoenstadt,
2008)
(Arthur Schoenstadt,
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%+UK T,+-+%(+(Arthur Schoenstadt, 2008)
Sering ditemukan di daerah Timur Tengah* Italia* Yunani*
dan Asia Selatan* Asia
Daerah endemis malaria
(iklim tr,"is)
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(P*(O-O'T,+-+%(+
Thalasemia-Kulithitam./0mem#a1aminimal
satugen
Thalasemia2AsiatenggaradanMediterania
$dari3',rang%inaadalah4arrierthalasemia
(Diana Curran,2010)
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EPIDEMI&L&5I DIIND&NESIA
6 7 $' dari $'' ,rang mem#a1a genthalasemia
Menurut Yaasan ThalasemiaInd,nesia ang #er,#at di Pusat
Thalasemia 8S%M hingga 9uli '':(Nusrat Madina,
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%)T(%% ,(O'-O)
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TIN5KATIN S8I& 5&?E8 $ @
5&?E8 -
HEM&5L&>INP&8TLAND
@B
CET
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*(F)% T,+-+%(+
(Cunningham dkk,
2010)
(Cunningham dkk,
2010)
(Cunningham dkk,
2010)
(Cunningham dkk,
2010)
*Cunningham dkk,
2010
Kelainan darah ang diturunkan se4ara genetikautosomal resesi#) dimana ter9adi ke4a4atandalam "r,duksi rantai gl,#in ("r,tein dalam sel
darah merah)
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T,+-+%(+
*cunningham dkk, 2010
SINTESISA>N&8MAL
E8IT8&P&ESIS TIDAK
ECEKTIC
HEM&LISIS
ANEMI
A
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enurut'ehlah danor!enstern/667$ insidensithalasemia &adakehamilandalam era!airas di&erkirakanterda&at dalam
dari 300 8 500wanita hamil
(Cunningham dkk, 2010)
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)*9*U )O+-
; 5EN
5L&>IN-
K8&M&S&M N&.$6
DIN
2
K8&M&S&M N&. $$
SAT< 5EN
PE8K8&M&S&
M
(Sylvieonglois dkk, 2008)
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(TO-O' T,+-+%(+
Thalasem
ia -
Thalasemia 2
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K-+%FK+%T,+-+%(+
8ANTAI5L&>IN
-THALASEMIA
2THALASEMIA
$. THALASEMIA -
MAY&8. H#H DISEASE3. THALASEMIA - MIN&8;. SILENT %A8IE8
$. THALASEMIA 2
MAY&8. THALASEMIA 2MIN&8
(Cunningham dkk, 2010)
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;()% T,+-+%(+