pediatric ophtalmologi-kuliah uncen.ppt

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    PEDIATRICPEDIATRIC

    OPHTALMOLOGIOPHTALMOLOGI

    Dr. Livia, SpMDr. Livia, SpM

    SMF I.K. MataSMF I.K. Mata

    RS Dian Harapan, JayapuraRS Dian Harapan, Jayapura

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    A. EMERIKSAAN MATA

    NEONATUS

    Tantangan dokter mata, dokter anak, dokter

    keluarga

    Gjl non spesifik, prkmbngn anak, modifikasi

    pemeriksaan Oftalmoskop direk/indirek, portable slit lamp

    Fenilefrin 1%; Siklopentolat 0,%; !omatropin

    "%; Tropi#amide 0,"% Opti# dis#, makula

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    Inspeksi ekstenal

    $upil dilatasi" mgg, refleks lambat,

    anisokoria 0,mm &"0%

    Oftalmoskopik

    'uang gelap,pd (()'&, prdr!n retina *0 s/d

    +% bbrp minggu kela!iran

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    B. EMERIKSAAN MATA ADA

    BAYI & ANAK

    isus - respon grkn, fiksasi, reaksi pupil, refleks

    kon.ergensi, grkn binokuler, prks satu per satu matasatuna diplester, reaksi penolakan,

    nistagmus/strabismus2

    'efraksi - sikloplegia utk atasi akomodasi, siklopentolat1%" 3 tts*0 mnt sblm pmrksn; inter.al mnt

    atropin 4alf mata 1%, "5* 3/!r "5* !r2

    60% !iperopia, % miopia,1% emetropia dan 10% ggn

    refraksi2

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    $emeriksaan segmen anterior dan posterior -

    7 Senter, loupe, slit lamp, oftalmoskop

    7 T8O, gonioskop

    7 'efleks fundus red reflex

    7 'efleks fo.ea

    7 Fundus perifer

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    C. KELAINAN KONGENITAL

    82 (O)9 :9T9

    79noftalmos

    7 oloboma iris, retina, koroid

    7 riptoftalmos, nanoftalmos, mikroftalmos

    882

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    9noftalmia

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    riptotalmus

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    :ikroftalmia = oloboma iris

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    $tosis (ilateral

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    $tosis >nilateral

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    8882 O'@

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    G)9>O:9 O@G

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    Glaukoma ongenital

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    orektopia

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    oloboma >.ea

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    2 )

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    atarak ongenital

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    'i S d

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    'iegers Sndrome

    (ilateral $eters 9nomal

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    (ilateral $eters 9nomal

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    882

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    (ergmeisters papilla

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    832 S9'9F O$T8>S

    7 Bipoplasi saraf optikus

    7 oloboma sentralis diskus morning glory

    syndrome

    32

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    9bnormalitas saraf optikus

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    oloboma 8ris = Saraf Optikus

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    ista okular

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    )imbal dermoid

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    D. EMERIKSAAN BAYI BUTA DGN

    HASIL MRKSN MATA &

    NEUROLOGIK YG NORMAL

    9maurosis kongenital leber

    ebutaan korteks

    $erlambatan pematangan .isual

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    E. MASALAH

    2

    ASCA LAHIR

    5 8nfeksi5 (enda asing

    5 'efraksi

    5 Strabismus5 'eaksi alergi

    5 elainan kongenital

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    12 Oftalmia @eonatorum

    5 8nf mata (()bktri, .rs, jmr, klamidia, b!n kimia

    5 9ntenatal #aretI infeksi genital ibu !ml5 Berpes genital aktifSe#tio Se#area

    A. Infeksi Klamidia

    Hi 9S plng srg, !r ke s/d 1+, dI pasti bdninklusi, lb! efktf tI eritromisin sistemik drpd tI

    topikal

    . !rauma kimia

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    au a a

    5 O/k prk nitrat, biasana pd !r 1 J "

    5 Sebaikna Cada! tertutup sekali pakai

    5 Hianjurkan eritromisin,tetrasiklin

    C. Infeksi akteri

    5 (iasana o/k Stap"# "aemop"ilus# streptokok#

    neiseria $O# pseudomonasinf pd !r ke " s/d 2

    $d inf klamidiaJ $Okedua ortu !rs jg diobati2

    %. Infeksi &irus

    5 Hitemukan giant sell, bdn inklusi, tI anti .irus

    "2 >.eitis pada 9nak

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    "2 >.eitis pada 9nak

    5 9simptomatik s/d trjd komplikasi, inf !bt, glaukoma,

    katarak, keratopati, dll

    5 9da !bngn dgn pnkt sistemik lainna mis- T(, rematoidartritis, infeksi lain

    5 TI sikloplegik J kortikosteroid topikal

    *2 'etinopati $rematuritas5 Fibroplasia retrolental, bilateral, stadium

    5 Faktor risiko KK usia gestasi, (()', asidosis, apneu,

    septikemia, transfusi dara!

    5 Skrining pada usia +0 mgg "5 + mgg stl! l!r bai dgn

    (() L 100 gr 0% ##lomdril

    5 Std 888 krioterapi atau fotokoagulasi

    + Gl k k it l

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    +2 Glaukoma kongenital

    5 Hpt berdiri sendiri atau bersama pen2lain

    5 Srg bilateral, fotofobia, lakrimasi, kekeru!an kornea,megalokornea, T8O

    5 (uftalmos

    2 )eukokoriaatarak, retinoblastoma, retinopati prematuritas,

    korpus .itreum primer !iperplastik persisten

    ' ti bl t

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    2 'etinoblastoma

    5 M s/d 0% mun#ul pd * t!n pertama

    5 *0% bilateraltmr gns fotoreseptor retina, jrg tapifatal

    5

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    '

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    HH2 Fibroplasia retrolental, $B$, #oats,

    endoftalmitis, displasia retina

    5 T3-

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    KELAINAN LENSA

    KATARAK5 9mbliopia

    5 1 - "0 kela!iran !idup

    Morfologi Infantile katarak

    5 @uklear katarak

    5 ortikal katarak

    5 )amelar/4onular katarak

    Anterior Katarak

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    Anterior Katarak

    5 9nterior polar katarak- kena kapsul dan korteks,

    lokasi sentral, ke#il, non progressif, .isus normal,btk piramid / #one

    Poterior Katarak

    5 $osterior lentikonus, $B$, astigmatisma,ambliopia

    5 $osterior subkapsular

    5 $osterior #orteks

    9nterior polar katarak

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    9nterior polar katarak

    atarak nuklear

    t k l l

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    atarak lamelar

    )entikonus posterior

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    )entikonus posterior

    atarak subkapsularis posterior

    !entuk lain katarak

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    !entuk lain katarak

    92 ?!ristmas tree #atara#t

    :otoni# dstrop!, Bpoparat!roidis$seudo!popara!roidism

    (2 ?erulean ?atara#t

    (lue dot #atara#t, HoCn sndrome, bilat

    ?2 :embranous #atara#t

    Trauma, intrauterin infeksi

    H2 >nilateral #atara#t

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    F2 ?atara#t dan infantile Glaukoma

    Lowes Syndrome-

    O#ulo#erebrorenal sndrome, katarak, glaukoma,pertumbu!an terlambat, !potonia, gangguan ginjal,

    amino a#iduria

    Rubella syndrome-Gangguan jantung, pendengaran, retardasi mental,

    strabismus, mikroptalmus, kornea keru!, glaukoma,

    katarak bilateral

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    Terapi Katarak

    Strategi- segera membersi!kan media refraksi

    untuk #ega! ambliopia ire.ersibel

    >nilateral #at K mgg, bilateral #at K 10 mgg

    " bln pertamanistagmus, strabismus,ambliopia

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    isus-*mm kekeru!an #entral, fiksasi

    Gerakan mata 'efleks fundus, .isus "0 / M0

    Teknik Operasi-

    5 Tidak perlu ekspresi nukleus5 Tidak perlu $!akoemulsif

    5 apsulotomi anterior, #utting, aspirasi / irigasi

    #orteks / nukleus, epitel dibaCa! kaps ant

    $ost #apsulotomi

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    p

    5 >sia "5* t!n8O)

    5 ?utting / su#tion

    5 ontraindikasi 8??