glaukoma-kongenital
DESCRIPTION
pptTRANSCRIPT
![Page 1: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/1.jpg)
Oleh : Atsilah Ulfah (1018011114)
Pembimbing : dr. Yusran, Sp.M
![Page 2: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/2.jpg)
Glaukoma kongenital
suatu glaukoma yang terjadi pada bayi atau anak-anak akibat penutupan bawaan dari sudut iridokorneal yang menghambat aliran dari aqeuous humor sehingga dapat meningkatkan tekanan intra okuler.
Kondisi ini progresif dan biasanya bilateral dan dapat merusak saraf optik.
![Page 3: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/3.jpg)
Klasifikasi Shaffer-Weiss Klasifikasi Anatomi Hoskins
![Page 4: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/4.jpg)
Glaukoma kongenital primer
-Late-developing primary congenital glaucoma
Glaukoma terkait anomali kongenital-Aniridia-Sindrom Sturge-Weber -Neurofibromatosis-Sindrom Pierre Robin-Homosistinuria-Goniodisgenesis (Sindrom Axenfeld, Sindrom Rieger,Anomali Pieter)-Sindrom Lowe-Mikrokornea-Mikrosperofakia-Rubella-Abnormalitas kromosom-Sindrom Rubistein-Taybi- Persistent hyperplastic primary vitreous
Glaukoma sekunder pada bayi-Retinopathy of prematurity-Tumor (Retinoblastoma, Juvenile xanthogranuloma)-Inflamasi-Trauma
![Page 5: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/5.jpg)
Isolated trabeculodysgenesis
- Flat iris insertion (anterior insertion, posterior insertion, mixed insertion)- Concave (wrap-around) iris insertion
- Unclassified
Iridotrabeculodysgenesis
- Anterior stromal defects (hypoplasia, hyperplasia)
- Anomalous iris vessels (persistence of tunica vasculosa lentis, anomalous superficial vessels)
- Structural anomalies (holes, colobomata, aniridia)Corneotrabeculodysgenesis
- Peripheral, e.g., Axenfeld’s anomaly
- Midperipheral, e.g., Rieger’s anomaly
- Central e.g., Peter’s anomaly, anterior staphyloma, AC cleavage syndrome, or posterior corneal ulcer of von Hippel
- Corneal size, e.g., microcornea or macrocornea
![Page 6: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/6.jpg)
1. airmata yang berlebihan (epifora)2. fotofobia3. spasme palpebra (blefarospasme)
![Page 7: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/7.jpg)
Epifora
Buphtalmos
![Page 8: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/8.jpg)
![Page 9: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/9.jpg)
1. buftalmos2. diameter kornea : diameter horizontal > 12 mm (megalokornea) sebelum tahun pertama
kehidupan sangat mendukung.3. abnormalitas pada salah satu lapisan kornea (membran Descement) yang bisa robek sehinggga menyebabkan edema
kornea.4. peningkatan tekanan intraokular5. abnormalitas pada pemeriksaan jaringan
trabekula6. cup diskus optik7. perubahan refraksi – terutama sekali miopia (penglihatan pendek)5. Pemeriksaan Klinis Pemeriksaan klinis pada glaukoma kongenital akut sebaiknya dilakukan
![Page 10: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/10.jpg)
1. Tonometri2. Gonioskopi3. Oftalmoskopi4. USG
![Page 11: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/11.jpg)
Goniotomi Trabekulotomi, Trabekulektomi, dilanjutkan
penggunakan obat antimetabolit seperti mitomisin
![Page 12: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/12.jpg)
![Page 13: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/13.jpg)
![Page 14: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/14.jpg)
Liesegang TJ, Skuta GL. Childhood Glaucoma in Glaucoma. American Academy of Opthalmology. Section 10. USA. 2005; p147-151.
Shaffer RN, Weiss DI: Congenital and Pediatric Glaucomas. St. Louis: CV Mosby, 1970.
Hoskins HD Jr, Hetherington J Jr, Shaffer RN, et al: Developmental glaucoma: diagnosis and classification. Proceedings of the New Orleans Academy of Ophthalmology Glaucoma Symposium. St. Louis: CV Mosby, 1981.
Hoskins HD Jr, Shaffer RN, Hetherington J Jr: Anatomical classification of the developmental glaucomas. Arch Ophthalmol 1984;102:1331-6.
Suhardjo, Hartono. Ilmu Kesehatan Mata. Yogyakarta : Bagian Ilmu Penyakit Mata Fakultas Kedokteran Universitas Gajah Mada, 2007.
Vaughan DG, Asbury T, Eva PR. Oftalmologi Umum. Ed 14th. Jakarta: Widya Medika, 2000.
Urban, Robert C. Primary Congenital Glaucoma. [diakses 8 Maret 2015]. Diunduh dari: http://www.emedicinehealth.com.
Masseen J, Kwon YH. Primary Congenital Glaucoma. 2005 [ diakses: 8 Maret 2015]. Diunduh dari: http://webeye.ophth.uiowa.edu.
Amoaku G, Browning G. Common Eye Diseases and Their Management. Third Edition. Springer-Verlag 2006; 12: 101-2.
Mandal AK, Chakrabarti D. Update on Congenital Glaucoma. Indian J Ophthalmol. 2011;59(Suppl1): S148-57.
Blanco AA, Wilson RP, Costa VP. Pediatric Glaucoma and Glaucoma Associated with Developmental Disorders. In Textbook: Handbook of Glaukoma. Martin Dunitz Ltd 2002;10: 147-51.
Yanoff M, Duker JS, Ausburger JJ. Ophthalmology 2nd Edition. Mosby Inc 2004: 1475-82.
Vavvas D, Grosskreutz C, Pasquale L. Congenital Glaucoma (Childhood). 2011. [diakses 8 Maret 2015] Diunduh dari: http://www.djo.harvard.edu/site.php?url=/patients/pi/416
Health Grades. Congenital Glaucoma. 2009. [diakses 8 Maret 2015] Diunduh dari: http://www.wrongdiagnosis.com/c/kongenital_glaukoma/intro.htm&rurl=translate.google.co.id&anno=2&usg=ALkJrhgUsUG9DqiGWDCuYv2x_NO7FlyDYw
![Page 15: Glaukoma-Kongenital](https://reader034.vdokumen.com/reader034/viewer/2022051020/563db90e550346aa9a999348/html5/thumbnails/15.jpg)